Lichen striatus
LS Β· Blaschko-linear dermatitis Β· blaschkitis (adult variant)
Lichen striatus is a benign, self-limiting linear inflammatory dermatosis predominantly affecting children, characterised by pink-to-flesh-coloured papules distributed along Blaschko lines on a limb. Adult-onset blaschkitis is a recognised variant. It is a common DDx for inflammatory linear verrucous epidermal naevus (ILVEN), Blaschko-linear lichen planus, linear psoriasis and incontinentia pigmenti. Resolution typically within 6-24 months with post-inflammatory hypo- or hyperpigmentation that may persist.
Pathogenesis
- Idiopathic; postulated post-zygotic mosaicism in skin clones, with cell-autonomous immunological reactivity following viral trigger or local trauma.
- Strong association with personal / family history of atopy.
- Distribution follows lines of Blaschko, reflecting ectodermal clonal patterns.
- Predominantly children 5-15 years; adult form (blaschkitis) less common.
Clinical features
- Linear band of 1-3 mm pink, flesh-coloured, or violaceous papules with fine scale.
- Unilateral; follows lines of Blaschko on a limb (more often lower limb), trunk or rarely face.
- Onset over days-weeks; reaches its maximum extent in weeks; persists 6-24 months.
- Asymptomatic or mildly pruritic.
- Resolution with post-inflammatory hypo- or hyperpigmentation, sometimes for years.
- Variants:
- Nail involvement (longitudinal ridging / onycholysis) β uncommon but recognised.
- Blaschkitis (adult variant) β recurrent eczematous, pruritic, vesicular.
Differentials
- Linear lichen planus β violaceous, polygonal, Wickham striae; more chronic.
- Inflammatory linear verrucous epidermal naevus (ILVEN) β congenital / very early; pruritic; verrucous, persistent.
- Linear psoriasis β silvery scale, Auspitz, personal / family history.
- Incontinentia pigmenti β early neonatal; X-linked dominant; vesicular β verrucous β hyperpigmented stages.
- Blaschko-linear lupus / morphoea.
- Linear porokeratosis β pathognomonic ridge / cornoid lamella; lifelong; SCC risk.
- Linear epidermal naevus (sebaceous, comedonicus) β congenital.
Investigations
- Clinical diagnosis in classic presentation.
- Skin biopsy in atypical / persistent cases: lichenoid interface dermatitis with focal parakeratosis; perivascular & periadnexal lymphocytic infiltrate.
- Photograph at baseline for monitoring.
Management
- Reassurance: self-limiting; counsel parents about months-long course and post-inflammatory pigment change.
- Topical:
- Emollients.
- Low-potency topical corticosteroid (hydrocortisone 1% to mid-potency mometasone) for active inflammation.
- Topical calcineurin inhibitors (tacrolimus 0.03% / 0.1%; pimecrolimus 1%) β first-line in children where steroid avoidance preferred.
- Sun protection during active phase; counsel about pigmentary residua.
- Persistent disease may benefit from narrowband UVB phototherapy.
- No systemic therapy usually required.
References
- Patrizi A et al. Lichen striatus: clinical and laboratory features in 115 children. Pediatr Dermatol. 2004;21:197-204.
- MΓΌller CSL et al. Lichen striatus and blaschkitis. J Dtsch Dermatol Ges. 2011;9:809-822.
- Hofer T. Lichen striatus in adults or "adult blaschkitis"? Dermatology. 2003;207:89-92.
- Tilly JJ et al. Lichenoid eruptions in children. J Am Acad Dermatol. 2004;51:606-624.
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